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Case Reports
. 2019 Jul 23;14(1):142.
doi: 10.1186/s13019-019-0968-x.

Non-syndromic aortic valve myxoma in a teen, cause of angina symptoms

Geoffrey Joseph Changwe  1 , Tao Zhang  1 , Haizhou Zhang  2 , Chengwei Zou  1
Affiliations
Case Reports

Non-syndromic aortic valve myxoma in a teen, cause of angina symptoms

Geoffrey Joseph Changwe et al. J Cardiothorac Surg. .

Abstract

Background: Cardiac myxoma, a common benign primary tumor of the heart can be categorized into syndromic (Carney Complex) and non-syndromic(isolated). Carney Complex associated myxomas can be found in any region and system (cardiac, cutaneous, osseous, genitalia), and may manifest at a tender age. On the contrary, non-syndromic cardiac myxomas are usually confined to the chambers, and symptoms often present from 5th decade of life. Aortic valve myxoma is a very unusual occurrence, and presentation in a teen is extremely rare.

Case report: We share a case of aortic valve myxoma, uncovered using echocardiography in a 16-year-old male, admitted with complaints of exertional chest pain, dyspnoea and systolic murmur. Patient underwent uneventful surgery for tumor excision, and discharged 6-days post operation.

Conclusion: Given the high risk of developing cardiogenic stroke, infective endocarditis, degenerative effects on aortic valve leaflets and possible sudden death, like many other centers, we advocate for immediate liquidation of aortic myxoma regardless of age and symptoms.

Keywords: Aortic valve myxoma; Cardiac myxoma; Carney complex; Non-syndromic.

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Conflict of interest statement

The authors declare that they have no competing interests.

Figures

Fig. 1
Fig. 1
Panels a & d, pre/post operation echocardiography (white arrow-myxoma), b-aortotomy & c –myxoma
Fig. 2
Fig. 2
Pathological [morphologic] report of aortic myxoma
See this image and copyright information in PMC

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